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3, Приложение . 2021

Anomalous draining hepatic vein to the left atrium in patient after univentricular correction

Abstract

We describe a clinical case of a patient with unbalanced atrioventricular canal defect and transposed great vessels after usual staged surgical treatment: pulmonary banding, Glenn procedure, Fontain procedure. Unexplained hypoxemia occurred after every surgical stage. The patient was diagnosed with anomaly of inferior vena cava: azygos continuation and anomalous draining hepatic vein into the left atrium. After staged surgical treatment this anomalous hepatic vein caused right-to-left shunting with mild hypoxemia representing a rare case of combined systemic and pulmonary veins.

Keywords:hepatic vein anomalous drainage, inferior vena cava agenesis, hypoxemia

Funding. The study had no sponsor support.
Conflict of interest. The authors declare no conflict of interest.
For citation: Kalnoy P.S., Kazantsev K.B., Kardapoltsev L.V., Chernadyev S.A. Anomalous draining hepatic vein to the left atrium in patient after univentricular correction. Clinical and Experimental Surgery. Petrovsky Journal. 2021; 9 (3): 100-4. DOI: https://doi.org/10.33029/2308-1198-2021-9-3suppl-100-104 (in Russian)

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CHIEF EDITOR
CHIEF EDITOR
Sergey L. Dzemeshkevich
MD, Professor (Moscow, Russia)

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